Human–mouse cystic fibrosis transmembrane conductance regulator (CFTR) chimeras identify regions that partially rescue CFTR-ΔF508 processing and alter its gating defect | PNAS
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The Primary Folding Defect and Rescue of ΔF508 CFTR Emerge during Translation of the Mutant Domain | PLOS ONE
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Genes | Free Full-Text | Cystic Fibrosis Gene Therapy: Looking Back, Looking Forward | HTML
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Rescue of ΔF508-CFTR Trafficking via a GRASP-Dependent Unconventional Secretion Pathway: Cell
Cystic Fibrosis Is Associated with a Defect in Apical Receptor–Mediated Endocytosis in Mouse and Human Kidney | American Society of Nephrology
Frontiers | Adapting Proteostasis and Autophagy for Controlling the Pathogenesis of Cystic Fibrosis Lung Disease
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![PDF] A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. | Semantic Scholar](https://d3i71xaburhd42.cloudfront.net/936a80c756a5b1a497bfa73b7c7a05f1d36cfa8a/3-Figure1-1.png "PDF] A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. | Semantic Scholar")
PDF] A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. | Semantic Scholar
Phenotypic Characterization and Comparison of Cystic Fibrosis Rat Models Generated Using CRISPR/Cas9 Gene Editing - The American Journal of Pathology
Kcnn4 is a modifier gene of intestinal cystic fibrosis preventing lethality in the Cftr-F508del mouse | Scientific Reports
JCI - A mouse model for the delta F508 allele of cystic fibrosis.
Cystic Fibrosis Mouse Model
PDF) A mouse model for the cystic fibrosis ΔF508 mutation
ΔF508 in cystic fibrosis: willing but not able | Archives of Disease in Childhood
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Cystic fibrosis transmembrane conductance regulator - Wikipedia
Structure-Function Relationships of CFTR in Health and Disease: The Pancreas Story | Pancreapedia
